Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report

Authors

  • Mahmoud A. Kiblawi RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.
  • Alina Naeem RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.
  • Elham A. Al Attrash RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.
  • Subhranshu Kar RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.
  • B. K. M. Goud RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.

DOI:

https://doi.org/10.5195/ijms.2013.220

Keywords:

Congenital Heart Block, Systemic Lupus Erythematosus, Bradycardia, SS-A Antibodies

Abstract

Background: Complete Congenital Heart Block (CCHB) is a rare disease of the newborn that carries significant morbidity and mortality. CCHB can be diagnosed early or late in life. In newborns, it is usually associated with maternal autoantibodies or a congenital cardiac structural abnormality. The most common presentation of CCHB is bradycardia that can be diagnosed by an electrocardiogram.

Results: This is a case report of a male infant born to a mother with an autoimmune disease, Systemic Lupus Erythematosus (SLE), who was found to have third degree heart block at birth.

Conclusion: Early diagnosis and prompt management of the case is important for a better prog­nosis and prevention of associated complications. Neonates with CCHB should be managed at a tertiary care center and the only definite treatment is insertion of a pacemaker. Moreover, prenatal diagnosis and specific obstetric counseling of pregnant women with SLE along with careful monitoring with serial ultrasonography and echocardiography are of paramount importance in prevention of the disease in subsequent offspring.

Author Biography

Mahmoud A. Kiblawi, RAK Medical College, RAK Medical and Health Sciences University, Ras Al Khaimah, United Arab Emirates.

Mahmoud Ahmed Kiblawi, recently graduated from a MBBS program at RAK Medical and Health Sciences University, Ras Al Khaimah, UAE, where he was honored thrice for best academic performance.

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Published

2013-12-31

How to Cite

Kiblawi, M. A., Naeem, A., Al Attrash, E. A., Kar, S., & Goud, B. K. M. (2013). Complete Congenital Heart Block in a Newborn Associated with Maternal Systemic Lupus Erythematosus: A Case Report. International Journal of Medical Students, 1(3), 128–131. https://doi.org/10.5195/ijms.2013.220

Issue

Section

Case Report

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